C6630Level 10
Malignant Melanotic Peripheral Nerve Sheath Tumor of the Mediastinum
**Semantic type:** Neoplastic Process
**Definition:** A rare variant of malignant peripheral nerve sheath tumor that arises from the mediastinum. It is characterized by the presence of malignant cells that contain melanin.
**Synonyms:** - Malignant Mediastinal Melanocytic Peripheral Nerve Sheath Tumor - Malignant Melanocytic Peripheral Nerve Sheath Tumor of Mediastinum - Mediastinal Melanocytic MPNST
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