Papillary Intralymphatic Angioendothelioma

**Semantic type:** Neoplastic Process

**Definition:** A rare, intermediate and rarely metastasizing blood vessel neoplasm that most often affects the skin and soft tissue of the extremities and manifests as a slow-growing induration, nodule, or plaque. Rare cases have been described in the spleen, tongue, and testis as well. It is characterized by the presence of lymphatic-like vascular channels and papillary endothelial proliferation.

**Synonyms:** - Dabska Tumor - Dabska tumor - Endovascular papillary angioendothelioma - Malignant Endothelial Papillary Angioendothelioma - PILA - Papillary Endovascular Angioendothelioma