Ornithine Carbamoyltransferase, Mitochondrial

**Semantic type:** Amino Acid, Peptide, or Protein|Enzyme

**Definition:** Ornithine carbamoyltransferase, mitochondrial (354 aa, ~40 kDa) is encoded by the human OTC gene. This protein plays a role in the metabolism of ornithine.

**Synonyms:** - EC 2.1.3.3 - OTCase - Ornithine Transcarbamylase