EBV-Positive T-Cell/NK-Cell Lymphoproliferative Disorder of Childhood

**Semantic type:** Neoplastic Process

**Definition:** An Epstein-Barr virus-associated mature T-cell/NK-cell lymphoproliferative group of disorders affecting children. It occurs with increased frequency in Asians and Native Americans. It includes the systemic EBV-positive T-cell lymphoma of childhood and the hydroa vacciniforme lymphoproliferative disorder.

**Synonyms:** - EBV-Positive T-Cell Lymphoproliferative Disease of Childhood - EBV-Positive T-Cell Lymphoproliferative Disorder of Childhood