Disseminated Juvenile Xanthogranuloma

**Semantic type:** Neoplastic Process

**Definition:** Juvenile xanthogranuloma disseminated to extracutaneous sites including mucosal surfaces, lung, central nervous system, pituitary, lymph nodes, eye, liver, and bone marrow. It is characterized by the presence of lipid-laden, foamy histiocytes and Touton-type giant cells forming nodules in the affected anatomic sites.

**Synonyms:** - Disseminated JXG - Disseminated JXG