Mucopolysaccharidosis Type I

**Semantic type:** Disease or Syndrome

**Definition:** The most common type of mucopolysaccharidosis. It is inherited in an autosomal recessive pattern. It comprises a group of lysosomal storage diseases which includes the most severe form (Hurler syndrome) and the mildest form (Scheie syndrome).

**Synonyms:** - MPS I - Mucopolysaccharidosis I