Systemic Mastocytosis with an Associated Myeloid Neoplasm

**Semantic type:** Neoplastic Process

**Definition:** A disorder characterized by systemic infiltration of internal organs by aggregates of clonal mast cells and the presence of a clonal non-mast cell myeloid neoplasm (e.g., myelodysplastic syndrome, myeloproliferative neoplasm, and acute myeloid leukemia).

**Synonyms:** - SM-AHN - SM-AHNMD - SM-AMN - Systemic Mastocytosis with Associated Clonal Hematological non-Mast-Cell Lineage Disease - Systemic Mastocytosis with Associated Clonal Hematological non-Mast-Cell Lineage Disease - Systemic Mastocytosis with an Associated Hematologic Neoplasm - Systemic Mastocytosis with an Associated Hematological Neoplasm (SM-AHN) - Systemic mastocytosis with AHNMD - Systemic mastocytosis with associated hematological clonal non-mast cell disorder