Sickle Beta 0 Thalassemia

**Semantic type:** Disease or Syndrome

**Definition:** A form of sickle cell thalassemia characterized by the absence of hemoglobin A. Patients usually have severe anemia identical to that seen in sickle cell disease.

**Synonyms:** - Hb S Beta 0 Thalassemia - Hemoglobin S Beta 0 Thalassemia - S Beta 0 Thalassemia - Sickle Beta Zero Thalassemia