Pulmonary Valve Atresia with Ventricular Septal Defect

**Semantic type:** Disease or Syndrome

**Definition:** Pulmonary valve atresia associated with the presence of a large ventricular septal defect. It may be a severe form of tetralogy of Fallot.

**Synonyms:** - Pulmonary Atresia with Ventricular Septal Defect