Peroxisome-Targeting Signal 1 Receptor

**Definition:** A cytoplasmic receptor and peroxin that contains a series of TETRATRICOPEPTIDE REPEATS and binds to PEROXISOME TARGETING SIGNAL 1 (SKL-type). It is essential for protein import into PEROXISOMES; mutations in the PEX5 gene are associated with PEROXISOMAL DISORDERS such as ZELLWEGER SYNDROME.

**Tree numbers:** - D12.776.157.635.750

**Synonyms:** - PTS1 Receptor - PTS1 Receptors - Peroxin PEX5 - Peroxisomal Biogenesis Factor 5 - Peroxisome Receptor 1 - Peroxin-5