Hamman-Rich Syndrome

**Definition:** Acute idiopathic interstitial pneumonitis characterized by diffuse PULMONARY ALVEOLI damage with uniform edematous connective tissue proliferation. It is often associated with extensive fibroblastic distortion of the lung parenchyma and leads to ADULT RESPIRATORY DISTRESS SYNDROME in later stages.

**Tree numbers:** - C08.381.483.652.500.500

**Synonyms:** - Acute Interstitial Pneumonia - Acute Interstitial Pneumonitis - Hamman-Rich Disease