Idiopathic Pulmonary Fibrosis

**Definition:** A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.

**Tree numbers:** - C08.381.483.652.500

**Synonyms:** - Cryptogenic Fibrosing Alveolitis - Pulmonary Fibrosis, Idiopathic - Fibrosing Alveolitis, Cryptogenic - Fibrocystic Pulmonary Dysplasia - Idiopathic Fibrosing Alveolitis, Chronic Form