Ichthyosiform Erythroderma, Congenital

**Definition:** Designation for several severe forms of ichthyosis, present at birth, that are characterized by hyperkeratotic scaling. Infants may be born encased in a collodion membrane which begins shedding within 24 hours. This is followed in about two weeks by persistent generalized scaling. The forms include bullous (HYPERKERATOSIS, EPIDERMOLYTIC), non-bullous (ICHTHYOSIS, LAMELLAR), wet type, and dry type.

**Tree numbers:** - C16.131.831.512.400 - C16.320.850.400 - C16.614.492.400 - C17.800.428.333.250 - C17.800.804.512.400 - C17.800.827.400

**Synonyms:** - Erythroderma, Congenital Ichthyosiform - Congenital Ichthyosiform Erythroderma