Ichthyosis, Lamellar

**Definition:** A chronic, congenital ichthyosis inherited as an autosomal recessive trait. Infants are usually born encased in a collodion membrane which sheds within a few weeks. Scaling is generalized and marked with grayish-brown quadrilateral scales, adherent at their centers and free at the edges. In some cases, scales are so thick that they resemble armored plate.

**Tree numbers:** - C16.131.831.512.400.410 - C16.320.850.400.410 - C16.614.492.400.410 - C17.800.428.333.250.410 - C17.800.804.512.400.410 - C17.800.827.400.410

**Synonyms:** - Erythroderma Ichthyosiforme, Nonbullous - Congenital Nonbullous Ichthyosiform Erythroderma - Nonbullous Congenital Ichthyosiform Erythroderma - Ichthyosiform Erythroderma, Nonbullous Congenital - Nonbullous Congenital Lamellar Ichthyosis - Congenital Ichthyosiform Erythroderma, Nonbullous - Lamellar Ichthyosis - Ichthyoses, Lamellar - Lamellar Ichthyoses