Hyperglycinemia, Nonketotic

**Definition:** An autosomal recessive metabolic disorder caused by deficiencies in the mitochondrial GLYCINE cleavage system.

**Tree numbers:** - C10.228.140.163.100.375 - C16.320.565.100.477 - C16.320.565.189.375 - C18.452.132.100.375 - C18.452.648.100.477 - C18.452.648.189.375

**Synonyms:** - Non-ketotic Hyperglycinemia - Nonketotic Hyperglycinemia - Glycine Encephalopathy