IgG4-Positive Primary Cutaneous Marginal Zone Lymphoproliferative Disorder

**Semantic type:** Neoplastic Process

**Definition:** A primary cutaneous marginal zone lymphoproliferative disorder characterized by the presence of class-switched immunoglobulin heavy chain expressing IgG4.

**Synonyms:** - IgG4 Positive Primary Cutaneous Marginal Zone Lymphoproliferative Disorder