SMARCB1-Deficient Sinonasal Adenocarcinoma

**Semantic type:** Neoplastic Process

**Definition:** An SWI/SNF-deficient sinonasal carcinoma characterized by inactivating mutation of SMARCB1 gene. It usually affects the nasal sinuses. It is composed of malignant epithelial cells with a predominantly oncocytoid/plasmacytoid morphology and prominent glandular formations.

**Synonyms:** - Sinonasal SMARCB1-Deficient Adenocarcinoma