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C201733Level 6

Beta-Hexosaminidase Subunit Alpha

**Semantic type:** Amino Acid, Peptide, or Protein|Enzyme

**Definition:** Beta-hexosaminidase subunit alpha (529 aa, ~61 kDa) is encoded by the human HEXA gene. This protein is involved in the hydrolysis of molecules containing terminal N-acetyl hexosamines, including GM2 gangliosides.

**Synonyms:** - Beta-Hexosaminidase Alpha-Subunit - Beta-N-Acetylhexosaminidase Subunit Alpha - EC 3.2.1.52 - HEXA - Hexosaminidase Subunit A - Hexosaminidase Subunit Alpha - N-Acetyl-Beta-Glucosaminidase Subunit Alpha

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