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C203945Level 6

Peptide-N(4)-(N-Acetyl-Beta-Glucosaminyl)Asparagine Amidase

**Semantic type:** Amino Acid, Peptide, or Protein|Enzyme

**Definition:** Peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase (654 aa, ~74 kDa) is encoded by the human NGLY1 gene. This protein is involved in catalyzing the deglycosylation of misfolded or denatured N-linked glycoproteins.

**Synonyms:** - EC 3.5.1.52 - N-Glycanase 1 - NGLY1 - PNGase - Peptide:N-Glycanase - hPNGase

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