Intravascular Large B-Cell Lymphoma

**Semantic type:** Neoplastic Process

**Definition:** A rare extranodal B-cell non-Hodgkin lymphoma, characterized by the presence of lymphoma cells exclusively in the lumina of small vessels, particularly capillaries. This is an extremely aggressive lymphoma which responds poorly to chemotherapy. (WHO, 2001)

**Synonyms:** - Angiotropic Large Cell Lymphoma - Angiotropic Lymphoma - Angiotropic lymphoma - IVLBCL - Intravascular B-Cell Lymphoma - Intravascular B-cell lymphoma - Intravascular large B-cell lymphoma - Malignant Angioendotheliomatosis