Dermatofibrosarcoma Protuberans

**Semantic type:** Neoplastic Process

**Definition:** A low grade fibroblastic neoplasm presenting as a nodular cutaneous mass, most often on the trunk and the proximal extremities. The tumor diffusely infiltrates the dermis and the subcutaneous tissues. It is considered a locally aggressive neoplasm, which often recurs but rarely metastasizes.

**Synonyms:** - DFSP - Dermatofibrosarcoma - Dermatofibrosarcoma - Dermatofibrosarcoma protuberans, NOS - dermatofibrosarcoma protuberans