Dysplastic Cerebellar Gangliocytoma

**Semantic type:** Neoplastic Process

**Definition:** A benign, WHO grade I cerebellar mass, which occurs in young adults and is composed of dysplastic ganglion cells. It is the major CNS manifestation of Cowden disease, an autosomal dominant condition that causes a variety of hamartomas and neoplasms.

**Synonyms:** - Dysplastic Cerebellar Gangliocytoma (Lhermitte-Duclos Disease) - Dysplastic Gangliocytoma of Cerebellum - Dysplastic Gangliocytoma of the Cerebellum - Dysplastic gangliocytoma of cerebellum (Lhermitte-Duclos) - Lhermitte-Duclos Disease