Systemic Hydroa Vacciniforme Lymphoproliferative Disorder

**Semantic type:** Neoplastic Process

**Definition:** Hydroa vacciniforme lymphoproliferative disorder characterized by severe clinical course and associated with fever, lymph node involvement, and involvement of internal organs by EBV-positive T-cells and NK-cells. It usually affects Asian and Latin American individuals.

**Synonyms:** - Systemic HV LPD - Systemic HV-LPD