Hydroa Vacciniforme Lymphoproliferative Disorder

**Semantic type:** Neoplastic Process

**Definition:** A rare, EBV-positive cutaneous T-cell lymphoproliferative disorder, composed of CD8 positive cytotoxic T-lymphocytes. It affects children, almost exclusively in Latin America and Asia. Patients present with papulovesicular skin lesions, clinically resembling hydroa vacciniforme, in areas of sun-exposed skin.

**Synonyms:** - HV LPD - HV-LPD - HV-Like LPD - HV-Like Lymphoma - Hydroa Vacciniforme-Like Cutaneous T-Cell Lymphoma - Hydroa Vacciniforme-Like Lymphoma - Hydroa Vacciniforme-Like Lymphoma - Hydroa Vacciniforme-Like Lymphoproliferative Disorder - Hydroa vacciniforme-like lymphoma