C3017Level 9
Ependymoma
**Semantic type:** Neoplastic Process
**Definition:** A WHO grade 2, slow growing tumor of children and young adults, usually located intraventricularly. It is the most common ependymal neoplasm. It often causes clinical symptoms by blocking cerebrospinal fluid pathways. Key histological features include perivascular pseudorosettes and ependymal rosettes. (WHO)
**Synonyms:** - CNS, ependymoma - Ependymoma, NOS - Ependymoma, NOS - WHO Grade 2 Ependymal Neoplasm - WHO Grade 2 Ependymal Tumor - WHO Grade II Ependymal Neoplasm - WHO Grade II Ependymal Tumor - ependymoma
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